Sign Up for a Free Account

Absence status epilepticus with perioral myoclonia (EEG)

From the EEG of a 23-year-old woman while in perioral myoclonia absence status epilepticus. She was mildly confused with continuous perioral twitching. This ended with a GTCS. Initial presentation at age 11 years was with GTCS. Absences with perioral myoclonia were noted at the same time and were diagnosed as focal motor seizures. (Used with permission from: Panayiotopoulos CP. A Clinical Guide to Epileptic Syndromes and Their Treatment. Revised 2nd ed. London: Springer, 2010.)

Associated Disorders

  • Epilepsy with myoclonic absences
  • Facial (perioral and or eyebrow) myoclonia with absences
  • Perioral myoclonia with absences